Systemic Mastocytosis: An Intriguing Disorder
نویسندگان
چکیده
منابع مشابه
گزارش یک مورد بیماری نادر پسودوگزانتوماتوس ماستوسیتوزیس
Diffuse cutaneous mastocytosis is very rare variety mast-cell disorder which is called peseudoxanthomatous mastocytosis. Our case was a man who was eighteen years old. He suffered from yellow papules on the neck, extremities , axillary and groins. The appearance of large blisters following ...
متن کاملDiagnostic value of tryptase in anaphylaxis and mastocytosis.
Serum (or plasma) levels of total and mature tryptase measurements are recommended in the diagnostic evaluation of systemic anaphylaxis and systemic mastocytosis, but their interpretation must be considered in the context of a complete workup of each patient. Total tryptase levels generally reflect the increased burden of mast cells in patients with all forms of systemic mastocytosis (indolent ...
متن کاملماستوسیتوزیس و بهترین شیوه‌های درمانی آن
Mastocytosis most frequently manifests in the skin, so most often is diagnosed by dermatologists at first. Low threshold in clinical suspicion helps early detection of these cases. Cutaneous mastocytosis is an increase of cutaneous mast cells without known underlying disease or inflammatory infiltrate. A skin biopsy with staining specific for mast cells (toluidine blue, Wright-Giemsa) and trypt...
متن کاملSystemic Mastocytosis with Smoldering Multiple Myeloma: Report of a Case
Systemic mastocytosis (SM) is a disease characterized by a clonal infiltration of mast cells affecting various tissues of the body. It is grouped into six different subtypes according to the World Health Organization classification. It is called indolent systemic mastocytosis (ISM) when there is no evidence of end organ dysfunction, while the presence of end organ dysfunction defines aggressive...
متن کاملAnaesthetic management of systemic mastocytosis.
Systemic mastocytosis is an uncommon disorder of mast cell proliferation in connective tissues. Mast cell degranulation may occur on exposure to various stimuli and drugs. The release of histamine, heparin and vasoactive substances such as prostaglandin D2 may cause severe hypotension and other anaphylactoid manifestations. Anaesthetic management should include perioperative stabilization of ma...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
عنوان ژورنال:
دوره شماره
صفحات -
تاریخ انتشار 2017